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World Top 100 Biopharmaceutical Companies List by Market Cap as of August 2026

World Top 100 Biopharmaceutical Companies List by Market Cap as of August 2026, World Biggest 100 Biopharmaceutical Companies by Market Cap, World Largest 100 Biopharmaceutical Companies in the World by market cap as of August 2026.

Metatag Title
World Top Biopharmaceutical Companies 2026
Metatag Abstract
World Largest Biopharmaceutical Companies by Market Cap in 2026, World Top Biopharmaceutical Companies by Market Cap in 2026.
  1. Immunovant

    World Rank (Aug-2026)
    2,458
    Market Cap (Aug-2026)
    8.638 Billion USD
    World Rank (Jan-05-2024)
    2,674
    Market Cap (Jan-05-2024)
    5.626 Billion USD
    World Rank (Jul-30-2023)
    4,418
    Market Cap (Jul-30-2023)
    2.942 Billion USD
    World Rank (Dec-25-2022)
    7,090
    Market Cap (Dec-25-2022)
    1.328 Billion USD
    World Rank (Jan-07-2022)
    9,880
    Market Cap (Jan-07-2022)
    0.92 Billion USD
    Annual Net Income in USD
    -506 Million USD
    Annual Results for Period Ending
    For year ending March-2026
    Headquarters Country
    Company Profile
    Immunovant is a Clinical Stage Biopharmaceutical company. It is focused on enabling normal lives for patients with autoimmune diseases. The headquarters is in USA.
  2. Eidos Therapeutics

    World Rank (Aug-2026)
    2,624
    World Rank (Jan-05-2024)
    2,624
    World Rank (Jul-30-2023)
    2,624
    World Rank (Dec-25-2022)
    2,624
    World Rank (Jan-07-2022)
    2,624
    Annual Revenue in USD
    27 Million USD
    Annual Operating Income in USD
    -40 Million USD
    Annual Net Income in USD
    -38 Million USD
    Annual Results for Period Ending
    For year ending December-2019
    Headquarters Country
    Company Profile

    Eidos Therapeutics is a Biopharmaceutical company with headquarters is in California, USA.

    Eidos Therapeutics was acquired by BridgeBio Pharma Inc in 2021.

     

  3. Iveric Bio

    World Rank (Aug-2026)
    2,731
    World Rank (Jan-05-2024)
    2,731
    World Rank (Jul-30-2023)
    2,731
    Market Cap (Jul-30-2023)
    5.510 Billion USD
    World Rank (Dec-25-2022)
    4,099
    Market Cap (Dec-25-2022)
    2.983 Billion USD
    World Rank (Jan-07-2022)
    7,176
    Market Cap (Jan-07-2022)
    1.61 Billion USD
    Annual Operating Income in USD
    -190 Million USD
    Annual Net Income in USD
    -185 Million USD
    Annual Results for Period Ending
    For year ending December-2022
    Headquarters Country
    Company Profile

    Iveric Bio is an Innovative Biopharmaceutical company focused on the discovery and development of treatments for retinal diseases with significant unmet medical needs. Iveric Bio 163 employees as on 2022. The headquarters is in USA.

    Astellas Pharma Inc. (TSE: 4503) has completed the acquisition of IVERIC bio, Inc. (NASDAQ: ISEE) on July 11, 2023 and the acquisition price of the same was 5.9 billion USD.

  4. TG Therapeutics

    World Rank (Aug-2026)
    2,738
    Market Cap (Aug-2026)
    7.461 Billion USD
    World Rank (Jan-05-2024)
    4,673
    Market Cap (Jan-05-2024)
    2.728 Billion USD
    World Rank (Jul-30-2023)
    4,415
    Market Cap (Jul-30-2023)
    2.943 Billion USD
    World Rank (Dec-25-2022)
    7,601
    Market Cap (Dec-25-2022)
    1.180 Billion USD
    World Rank (Jan-07-2022)
    5,472
    Market Cap (Jan-07-2022)
    2.50 Billion USD
    Annual Revenue in USD
    616 Million USD
    Annual Operating Income in USD
    123 Million USD
    Annual Net Income in USD
    447 Million USD
    Annual Results for Period Ending
    For year ending December-2025
    Headquarters Country
    Company Profile
    TG Therapeutics is a Biopharmaceutical company. The company annual revenue is less than 1 million USD and 217 employees. The headquarters is in USA.
  5. Biocon

    World Rank (Aug-2026)
    2,848
    Market Cap (Aug-2026)
    7.055 Billion USD
    World Rank (Jan-05-2024)
    3,442
    Market Cap (Jan-05-2024)
    4.090 Billion USD
    World Rank (Jul-30-2023)
    3,712
    Market Cap (Jul-30-2023)
    3.746 Billion USD
    World Rank (Dec-25-2022)
    3,398
    Market Cap (Dec-25-2022)
    3.845 Billion USD
    World Rank (Jan-07-2022)
    2,935
    Market Cap (Jan-07-2022)
    5.76 Billion USD
    Annual Revenue in USD
    1,004 Million USD
    Annual Net Income in USD
    81 Million USD
    Annual Results for Period Ending
    Mar-2022 ending year
    Headquarters Country
    Stock Category
    Company Profile

    Biocon is India's largest Bio-pharmaceutical company with headquarters is in Bangalore, India. As on 2020, it has 12,000 employees and 1220 patents and 900 Registered Trademarks and they supply their products to 120 countries.

    Key therapeutic areas are diabetes, oncology, immunology, agriculture of innovation.

  6. Arena Pharmaceuticals

    World Rank (Aug-2026)
    2,949
    World Rank (Jan-05-2024)
    2,949
    World Rank (Jul-30-2023)
    2,949
    World Rank (Dec-25-2022)
    2,949
    World Rank (Jan-07-2022)
    2,949
    Market Cap (Jan-07-2022)
    5.74 Billion USD
    Annual Revenue in USD
    0 Million USD
    Annual Operating Income in USD
    -624 Million USD
    Annual Net Income in USD
    -616 Million USD
    Annual Results for Period Ending
    For year ending December-2021
    Headquarters Country
    Company Profile

    Bio-pharmaceutical company with headquarters is in California, USA.

  7. Mirum Pharmaceuticals

    World Rank (Aug-2026)
    3,000
    Market Cap (Aug-2026)
    6.535 Billion USD
    World Rank (Jan-05-2024)
    7,121
    Market Cap (Jan-05-2024)
    1.384 Billion USD
    World Rank (Jul-30-2023)
    8,800
    Market Cap (Jul-30-2023)
    0.988 Billion USD
    World Rank (Dec-25-2022)
    10,559
    Market Cap (Dec-25-2022)
    0.673 Billion USD
    World Rank (Jan-07-2022)
    13,731
    Market Cap (Jan-07-2022)
    0.48 Billion USD
    Annual Revenue in USD
    521 Million USD
    Annual Operating Income in USD
    -22 Million USD
    Annual Net Income in USD
    -23 Million USD
    Annual Results for Period Ending
    For year ending December-2025
    Headquarters Country
    Company Profile
    Mirum Pharmaceuticals is a Clinical Stage Biopharmaceutical company focused on clinical studies for the treatment of cholestatic diseases including primary sclerosing cholangitis (PSC), intrahepatic cholestasis of pregnancy (ICP) and primary biliary cholangitis (PBC). It is having 24 employees as on 2019. The headquarters is in USA.
  8. Belite Bio Inc

    World Rank (Aug-2026)
    3,042
    Market Cap (Aug-2026)
    6.405 Billion USD
    World Rank (Jan-05-2024)
    7,954
    Market Cap (Jan-05-2024)
    1.137 Billion USD
    World Rank (Jul-30-2023)
    11,043
    Market Cap (Jul-30-2023)
    0.656 Billion USD
    World Rank (Dec-25-2022)
    9,808
    Market Cap (Dec-25-2022)
    0.768 Billion USD
    Annual Operating Income in USD
    -84 Million USD
    Annual Net Income in USD
    -78 Million USD
    Annual Results for Period Ending
    For year ending December-2025
    Headquarters Country
    Company Profile
    Belite Bio Inc is a clinical stage biopharmaceutical drug development company focused on aging metabolic diseases including dry age related macular degeneration, liver disease and diabetes. The headquarters is in United States.
  9. Xenon Pharmaceuticals

    World Rank (Aug-2026)
    3,179
    Market Cap (Aug-2026)
    6.038 Billion USD
    World Rank (Jan-05-2024)
    3,922
    Market Cap (Jan-05-2024)
    3.464 Billion USD
    World Rank (Jul-30-2023)
    5,199
    Market Cap (Jul-30-2023)
    2.331 Billion USD
    World Rank (Dec-25-2022)
    4,829
    Market Cap (Dec-25-2022)
    2.382 Billion USD
    World Rank (Jan-07-2022)
    7,271
    Market Cap (Jan-07-2022)
    1.57 Billion USD
    Annual Revenue in USD
    32 Million USD
    Annual Net Income in USD
    -28 Million USD
    Annual Results for Period Ending
    Dec-2020 ending year
    Headquarters Country
    Company Profile
    Xenon Pharmaceuticals is a clinical stage biopharmaceutical company committed to developing innovative therapeutics to improve the lives of patients with neurological disorders. The headquarters is in Canada.
  10. PTC Therapeutics Inc.

    World Rank (Aug-2026)
    3,206
    Market Cap (Aug-2026)
    5.984 Billion USD
    World Rank (Jan-05-2024)
    5,486
    Market Cap (Jan-05-2024)
    2.120 Billion USD
    World Rank (Jul-30-2023)
    4,320
    Market Cap (Jul-30-2023)
    3.037 Billion USD
    World Rank (Dec-25-2022)
    4,471
    Market Cap (Dec-25-2022)
    2.661 Billion USD
    World Rank (Jan-07-2022)
    5,237
    Market Cap (Jan-07-2022)
    2.69 Billion USD
    Annual Revenue in USD
    1,731 Million USD
    Annual Operating Income in USD
    867 Million USD
    Annual Net Income in USD
    683 Million USD
    Annual Results for Period Ending
    For year ending December-2025
    Headquarters Country
    Company Profile

    PTC Therapeutics is a Commercial and Diversified Biopharmaceutical company. It operates offices and research labs in more than 20 countries and occupy a business footprint in more than 50 countries around the world. It is a having 2,20,000 square feet in Hopewell, New Jersey. The headquarters is in USA.

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