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World Top 100 Biotechnology Companies List by Market Cap as of August 2026

World Top 100 Biotechnology Companies List by Market Cap as of August 2026, World Biggest 100 Biotechnology Companies by Market Cap, World Largest 100 Biotechnology Companies in the World by market cap as of August 2026.

Metatag Title
World Top Biotechnology Companies in 2026
Metatag Abstract
World Largest Biotechnology Companies by Market Cap in 2026, World Top Biotechnology Companies by Market Cap in 2026.
  1. Pharma Mar

    World Rank (Aug-2026)
    6,162
    Market Cap (Aug-2026)
    2.102 Billion USD
    World Rank (Jan-05-2024)
    9,684
    Market Cap (Jan-05-2024)
    0.816 Billion USD
    World Rank (Jul-30-2023)
    10,987
    Market Cap (Jul-30-2023)
    0.662 Billion USD
    World Rank (Dec-25-2022)
    7,221
    Market Cap (Dec-25-2022)
    1.288 Billion USD
    World Rank (Jan-07-2022)
    8,857
    Market Cap (Jan-07-2022)
    1.11 Billion USD
    Annual Revenue in USD
    229 Million USD
    Annual Net Income in USD
    92 Million USD
    Annual Results for Period Ending
    Dec-2021 ending year
    Headquarters Country
    Company Profile
    Pharma Mar is a biopharmaceutical company focused on anti cancer drugs based on marine invertebrates. The company annual revenue is 269.9 million EUR, annual operating income is 155.9 million EUR, annual net income is 137.2 million EUR and total assets are 330 million EUR as on 2020. The headquarters is in Spain.
  2. Neuren Pharmaceuticals

    World Rank (Aug-2026)
    6,165
    Market Cap (Aug-2026)
    2.100 Billion USD
    World Rank (Jan-05-2024)
    5,527
    Market Cap (Jan-05-2024)
    2.090 Billion USD
    World Rank (Jul-30-2023)
    8,222
    Market Cap (Jul-30-2023)
    1.112 Billion USD
    World Rank (Dec-25-2022)
    10,227
    Market Cap (Dec-25-2022)
    0.715 Billion USD
    World Rank (Jan-07-2022)
    15,657
    Market Cap (Jan-07-2022)
    0.36 Billion USD
    Headquarters Country
  3. Genus

    World Rank (Aug-2026)
    6,183
    Market Cap (Aug-2026)
    2.087 Billion USD
    World Rank (Jan-05-2024)
    6,032
    Market Cap (Jan-05-2024)
    1.815 Billion USD
    World Rank (Jul-30-2023)
    5,563
    Market Cap (Jul-30-2023)
    2.094 Billion USD
    World Rank (Dec-25-2022)
    4,834
    Market Cap (Dec-25-2022)
    2.378 Billion USD
    World Rank (Jan-07-2022)
    3,804
    Market Cap (Jan-07-2022)
    4.11 Billion USD
    Annual Revenue in USD
    676 Million USD
    Annual Net Income in USD
    55 Million USD
    Annual Results for Period Ending
    Jun-2022 ending year
    Headquarters Country
    Company Profile
    Genus is a Animal Genetics company. The company is a breed better pigs and cattle for farmers so that they can produce high quality meat and milk more efficiently and sustainably. The headquarters is in UK.
  4. Aurinia Pharmaceuticals

    World Rank (Aug-2026)
    6,240
    Market Cap (Aug-2026)
    2.058 Billion USD
    World Rank (Jan-05-2024)
    7,666
    Market Cap (Jan-05-2024)
    1.213 Billion USD
    World Rank (Jul-30-2023)
    6,232
    Market Cap (Jul-30-2023)
    1.755 Billion USD
    World Rank (Dec-25-2022)
    10,850
    Market Cap (Dec-25-2022)
    0.644 Billion USD
    World Rank (Jan-07-2022)
    5,556
    Market Cap (Jan-07-2022)
    2.44 Billion USD
    Annual Revenue in USD
    35 Million USD
    Annual Net Income in USD
    -138 Million USD
    Annual Results for Period Ending
    Dec-2021 ending year
    Headquarters Country
    Company Profile
    Aurinia Pharmaceuticals is a Clinical Stage Biopharmaceutical company. The company developing in voclosporin, an investigational therapy for the treatment of lupus nephritis and other proteinuric diseases. The headquarters is in Canada.
  5. Jinyu Bio-Technology

    World Rank (Aug-2026)
    6,250
    Market Cap (Aug-2026)
    2.052 Billion USD
    World Rank (Jan-05-2024)
    6,350
    Market Cap (Jan-05-2024)
    1.660 Billion USD
    World Rank (Jul-30-2023)
    6,633
    Market Cap (Jul-30-2023)
    1.586 Billion USD
    World Rank (Dec-25-2022)
    6,652
    Market Cap (Dec-25-2022)
    1.464 Billion USD
    World Rank (Jan-07-2022)
    4,810
    Market Cap (Jan-07-2022)
    3.04 Billion USD
    Annual Revenue in USD
    258 Million USD
    Annual Net Income in USD
    56 Million USD
    Annual Results for Period Ending
    Dec-2021 ending year
    Headquarters Country
  6. GH Research PLC

    World Rank (Aug-2026)
    6,291
    Market Cap (Aug-2026)
    2.022 Billion USD
    World Rank (Jan-05-2024)
    16,085
    Market Cap (Jan-05-2024)
    0.284 Billion USD
    World Rank (Jul-30-2023)
    10,432
    Market Cap (Jul-30-2023)
    0.732 Billion USD
    World Rank (Dec-25-2022)
    12,316
    Market Cap (Dec-25-2022)
    0.507 Billion USD
    World Rank (Jan-07-2022)
    9,593
    Market Cap (Jan-07-2022)
    0.97 Billion USD
    Headquarters Country
    Company Profile
    GH Research PLC is a clinical stage biopharmaceutical company dedicated to transforming the treatment of psychiatric and neurological disorders. The headquarters is in Ireland.
  7. Stoke Therapeutics

    World Rank (Aug-2026)
    6,298
    Market Cap (Aug-2026)
    2.018 Billion USD
    World Rank (Jan-05-2024)
    16,842
    Market Cap (Jan-05-2024)
    0.245 Billion USD
    World Rank (Jul-30-2023)
    16,233
    Market Cap (Jul-30-2023)
    0.280 Billion USD
    World Rank (Dec-25-2022)
    15,180
    Market Cap (Dec-25-2022)
    0.327 Billion USD
    World Rank (Jan-07-2022)
    11,113
    Market Cap (Jan-07-2022)
    0.74 Billion USD
    Annual Revenue in USD
    184 Million USD
    Annual Operating Income in USD
    -21 Million USD
    Annual Net Income in USD
    -7 Million USD
    Annual Results for Period Ending
    For year ending December-2025
    Headquarters Country
    Company Profile
    Stoke Therapeutics is a Biotechnology company. The company estimated annual revenue is currently 7.9 million USD per year and has 44 employees as on 2019. The headquarters is in USA.
  8. Agios Pharmaceuticals

    World Rank (Aug-2026)
    6,312
    Market Cap (Aug-2026)
    2.004 Billion USD
    World Rank (Jan-05-2024)
    7,260
    Market Cap (Jan-05-2024)
    1.340 Billion USD
    World Rank (Jul-30-2023)
    6,950
    Market Cap (Jul-30-2023)
    1.477 Billion USD
    World Rank (Dec-25-2022)
    6,594
    Market Cap (Dec-25-2022)
    1.485 Billion USD
    World Rank (Jan-07-2022)
    6,755
    Market Cap (Jan-07-2022)
    1.77 Billion USD
    Annual Revenue in USD
    54 Million USD
    Annual Operating Income in USD
    -472 Million USD
    Annual Net Income in USD
    -413 Million USD
    Annual Results for Period Ending
    For year ending December-2025
    Headquarters Country
    Company Profile
    Bio-pharmaceutical company with headquarters is in Massachusetts, USA.
  9. Shanghai Medicilon

    World Rank (Aug-2026)
    6,393
    Market Cap (Aug-2026)
    1.967 Billion USD
    World Rank (Jan-05-2024)
    7,605
    Market Cap (Jan-05-2024)
    1.231 Billion USD
    World Rank (Jul-30-2023)
    6,784
    Market Cap (Jul-30-2023)
    1.534 Billion USD
    World Rank (Dec-25-2022)
    4,906
    Market Cap (Dec-25-2022)
    2.333 Billion USD
    World Rank (Jan-07-2022)
    3,714
    Market Cap (Jan-07-2022)
    4.23 Billion USD
    Annual Revenue in USD
    170 Million USD
    Annual Net Income in USD
    41 Million USD
    Annual Results for Period Ending
    Dec-2021 ending year
    Headquarters Country
  10. Taysha Gene Therapies Inc.

    World Rank (Aug-2026)
    6,450
    Market Cap (Aug-2026)
    1.939 Billion USD
    World Rank (Jan-05-2024)
    15,206
    Market Cap (Jan-05-2024)
    0.329 Billion USD
    World Rank (Jul-30-2023)
    25,824
    Market Cap (Jul-30-2023)
    0.044 Billion USD
    World Rank (Dec-25-2022)
    20,293
    Market Cap (Dec-25-2022)
    0.130 Billion USD
    World Rank (Jan-07-2022)
    14,513
    Market Cap (Jan-07-2022)
    0.42 Billion USD
    Annual Revenue in USD
    10 Million USD
    Annual Operating Income in USD
    -110 Million USD
    Annual Net Income in USD
    -109 Million USD
    Annual Results for Period Ending
    For year ending December-2025
    Headquarters Country
    Company Profile
    Taysha Gene Therapies is a Biotechnology company focused on discovering, developing and commercializing gene therapies for the treatment of monogenic diseases of the central nervous system (CNS) both in rare and large patient populations. It is having 10 employees as on 2019. The headquarters is in USA.

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